Ewing sarcoma/peripheral primitive neuroectodermal tumor of the kidney: report of two cases
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چکیده
Ewing sarcoma/peripheral primitive neuroectodermal tumor (ES/pPNET) arising in the kidney is very rare, and only a few cases have been reported. Here we present two cases of renal ES/pPNET with different prognosis. Both patients underwent radical nephrectomy. One patient had complex EWSR1 gene chromosome translocation, high Ki-67 proliferative index and died of metastatic disease 2 months after surgery. The other patient had conventional EWSR1 gene translocation, low Ki-67 proliferative index and is alive with no evidence of disease after 4 year follow-up.
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تاریخ انتشار 2016